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1. headache has developed in temporal relation to the onset of the non-vascular intracranial disorder
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2. either or both of the following:
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b) headache has significantly improved in parallel with improvement in the non-vascular intracranial disorder
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3. headache has characteristics typical for the nonvascular intracranial disorder
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4. other evidence exists of causation
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Headache
© 2013 American Headache Society
Spontaneous Low Pressure, Low CSF Volume Headaches:Spontaneous CSF Leaks
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Bahram Mokri, MD
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Radioisotope Cisternography.
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Indium-111 is the radioisotope of choice.
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It is introduced intrathecally (IT) via an LP and its dynamics are followed by sequential scanning at various intervals of up to 24 or even 48 hours.
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Normally after 24 hours, though often earlier, ample radioactivity can be detected over the cerebral convexities while no activity outside the dural sac is noted, unless there has been inadvertent injection of part of the radioisotope extradurally or if some of the IT-injected radioisotope has extravasated through the dural puncture site.
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In CSF leaks, the following should be expected:
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1. The radioactivity should not extend much beyond the basal cisterns, and therefore, at 24 or even at 48 hours, there is paucity of activity over the cerebral convexities (Fig. 4A,B).
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34-36 Although an ¡Èindirect evidence,¡É this is the most common and most reliable
cisternographic abnormality in active CSF leaks.
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This is particularly helpful when the clinical and MRI findings are atypical, insufficient, or unconvincing and, therefore, leaving the clinician with a fundamental uncertainty about the diagnosis.
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2. Presence of parathecal activity as a ¡Èdirect evidence¡É of leak pointing to the level or the approximate site of the leak (Fig. 4B,C), unfortunately, is far less commonly noted than paucity of activity over cerebral convexities.
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 Of note, meningeal diverticula – if large enough – may appear as foci of parathecal activity and sometimes may not be reliably distinguished from actual sites of leak.
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Computed tomography myelography (CTM) is frequently needed to advance the workup appropriately, not only to enable this differentiation but to confirm the actual site of the leak.
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Meningeal diverticula may or may not be the actual site of the leak even when they are large.
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3. Early appearance of radioactivity in the kidneys and urinary bladder (in less than 4 hours vs 6-24 hours) is a fairly common ¡Èindirect evidence,¡É indicating that the IT-introduced radioisotope has extravasated and entered the venous system quickly with subsequent early renal clearance and early appearance in the urinary bladder.
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This finding, however, is of limited reliability and can be affected by partial extradural radioisotope injection or perhaps even more commonly by extravasation of IT-injected radioisotope from the dural puncture site back to the epidural tissues.
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This is identical to the mechanism involved in postdural puncture headaches.
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